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Q75N90 Proteins EGF-like domain Repeats
Uniprot ID:Q75N90
Protein name: Fibrillin-3 [Cleaved into: Fibrillin-3 C-terminal peptide]
Gene : FBN3 KIAA1776
Protein Family:Fibrillin family
Squence Length : 2809
Sequnce
>Q75N90 2810 MTLEGLYLARGPLARLLLAWSALLCMAGGQGRWDGALEAAGPGRVRRRGSPGILQGPNVCGSRFHAYCCPGWRTFPGRSQCVVPICRRACGEGFCSQPNLCTCADGTLAPSCGVSRGSGCSVSCMNGGTCRGASCLCQKGYTGTVCGQPICDRGCHNGGRCIGPNRCACVYGFMGPQCERDYRTGPCFGQVGPEGCQHQLTGLVCTKALCCATVGRAWGLPCELCPAQPHPCRRGFIPNIHTGACQDVDECQAVPGLCQGGSCVNMVGSFHCRCPVGHRLSDSSAACEDYRAGACFSVLFGGRCAGDLAGHYTRRQCCCDRGRCWAAGPVPELCPPRGSNEFQQLCAQRLPLLPGHPGLFPGLLGFGSNGMGPPLGPARLNPHGSDARGIPSLGPGNSNIGTATLNQTIDICRHFTNLCLNGRCLPTPSSYRCECNVGYTQDVRGECIDVDECTSSPCHHGDCVNIPGTYHCRCYPGFQATPTRQACVDVDECIVSGGLCHLGRCVNTEGSFQCVCNAGFELSPDGKNCVDHNECATSTMCVNGVCLNEDGSFSCLCKPGFLLAPGGHYCMDIDECQTPGICVNGHCTNTEGSFRCQCLGGLAVGTDGRVCVDTHVRSTCYGAIEKGSCARPFPGTVTKSECCCANPDHGFGEPCQLCPAKDSAEFQALCSSGLGITTDGRDINECALDPEVCANGVCENLRGSYRCVCNLGYEAGASGKDCTDVDECALNSLLCDNGWCQNSPGSYSCSCPPGFHFWQDTEICKDVDECLSSPCVSGVCRNLAGSYTCKCGPGSRLDPSGTFCLDSTKGTCWLKIQESRCEVNLQGASLRSECCATLGAAWGSPCERCEIDPACARGFARMTGVTCDDVNECESFPGVCPNGRCVNTAGSFRCECPEGLMLDASGRLCVDVRLEPCFLRWDEDECGVTLPGKYRMDVCCCSIGAVWGVECEACPDPESLEFASLCPRGLGFASRDFLSGRPFYKDVNECKVFPGLCTHGTCRNTVGSFHCACAGGFALDAQERNCTDIDECRISPDLCGQGTCVNTPGSFECECFPGYESGFMLMKNCMDVDECARDPLLCRGGTCTNTDGSYKCQCPPGHELTAKGTACEDIDECSLSDGLCPHGQCVNVIGAFQCSCHAGFQSTPDRQGCVDINECRVQNGGCDVHCINTEGSYRCSCGQGYSLMPDGRACADVDECEENPRVCDQGHCTNMPGGHRCLCYDGFMATPDMRTCVDVDECDLNPHICLHGDCENTKGSFVCHCQLGYMVRKGATGCSDVDECEVGGHNCDSHASCLNIPGSFSCRCLPGWVGDGFECHDLDECVSQEHRCSPRGDCLNVPGSYRCTCRQGFAGDGFFCEDRDECAENVDLCDNGQCLNAPGGYRCECEMGFDPTEDHRACQDVDECAQGNLCAFGSCENLPGMFRCICNGGYELDRGGGNCTDINECADPVNCINGVCINTPGSYLCSCPQDFELNPSGVGCVDTRAGNCFLETHDRGDSGISCSAEIGVGVTRASCCCSLGRAWGNPCELCPMANTTEYRTLCPGGEGFQPNRITVILEDIDECQELPGLCQGGDCVNTFGSFQCECPPGYHLSEHTRICEDIDECSTHSGICGPGTCYNTLGNYTCVCPAEYLQVNGGNNCMDMRKSVCFRHYNGTCQNELAFNVTRKMCCCSYNIGQAWNRPCEACPTPISPDYQILCGNQAPGFLTDIHTGKPLDIDECGEIPAICANGICINQIGSFRCECPAGFNYNSILLACEDVDECGSRESPCQQNADCINIPGSYRCKCTRGYKLSPGGACVGRNECREIPNVCSHGDCMDTEGSYMCLCHRGFQASADQTLCMDIDECDRQPCGNGTCKNIIGSYNCLCFPGFVVTHNGDCVDFDECTTLVGQVCRFGHCLNTAGSFHCLCQDGFELTADGKNCVDTNECLSLAGTCLPGTCQNLEGSFRCICPPGFQVQSDHCIDIDECSEEPNLCLFGTCTNSPGSFQCLCPPGFVLSDNGHRCFDTRQSFCFTRFEAGKCSVPKAFNTTKTRCCCSKRPGEGWGDPCELCPQEGSAAFQELCPFGHGAVPGPDDSREDVNECAENPGVCTNGVCVNTDGSFRCECPFGYSLDFTGINCVDTDECSVGHPCGQGTCTNVIGGFECACADGFEPGLMMTCEDIDECSLNPLLCAFRCHNTEGSYLCTCPAGYTLREDGAMCRDVDECADGQQDCHARGMECKNLIGTFACVCPPGMRPLPGSGEGCTDDNECHAQPDLCVNGRCVNTAGSFRCDCDEGFQPSPTLTECHDIRQGPCFAEVLQTMCRSLSSSSEAVTRAECCCGGGRGWGPRCELCPLPGTSAYRKLCPHGSGYTAEGRDVDECRMLAHLCAHGECINSLGSFRCHCQAGYTPDATATTCLDMDECSQVPKPCTFLCKNTKGSFLCSCPRGYLLEEDGRTCKDLDECTSRQHNCQFLCVNTVGAFTCRCPPGFTQHHQACFDNDECSAQPGPCGAHGHCHNTPGSFRCECHQGFTLVSSGHGCEDVNECDGPHRCQHGCQNQLGGYRCSCPQGFTQHSQWAQCVDENECALSPPTCGSASCRNTLGGFRCVCPSGFDFDQALGGCQEVDECAGRRGPCSYSCANTPGGFLCGCPQGYFRAGQGHCVSGLGFSPGPQDTPDKEELLSSEACYECKINGLSPRDRPRRSAHRDHQVNLATLDSEALLTLGLNLSHLGRAERILELRPALEGLEGRIRYVIVRGNEQGFFRMHHLRGVSSLQLGRRRPGPGTYRLEVVSHMAGPWGVQPEGQPGPWGQALRLKVQLQLL
Domains
DOMAIN 147 179 EGF-like 1 DOMAIN 185 237 TB 1 DOMAIN 247 288 EGF-like 2 calcium-binding DOMAIN 293 346 TB 2 DOMAIN 408 448 EGF-like 3 DOMAIN 449 488 EGF-like 4 calcium-binding DOMAIN 489 530 EGF-like 5 calcium-binding DOMAIN 531 571 EGF-like 6 calcium-binding DOMAIN 572 612 EGF-like 7 calcium-binding DOMAIN 618 670 TB 3 DOMAIN 682 723 EGF-like 8 calcium-binding DOMAIN 724 765 EGF-like 9 calcium-binding DOMAIN 766 805 EGF-like 10 calcium-binding DOMAIN 810 861 TB 4 DOMAIN 869 910 EGF-like 11 calcium-binding DOMAIN 915 966 TB 5 DOMAIN 986 1027 EGF-like 12 calcium-binding DOMAIN 1028 1070 EGF-like 13 calcium-binding DOMAIN 1071 1112 EGF-like 14 calcium-binding DOMAIN 1113 1154 EGF-like 15 calcium-binding DOMAIN 1155 1195 EGF-like 16 calcium-binding DOMAIN 1196 1237 EGF-like 17 DOMAIN 1238 1279 EGF-like 18 calcium-binding DOMAIN 1280 1320 EGF-like 19 calcium-binding DOMAIN 1321 1361 EGF-like 20 calcium-binding DOMAIN 1362 1403 EGF-like 21 calcium-binding DOMAIN 1404 1444 EGF-like 22 calcium-binding DOMAIN 1445 1485 EGF-like 23 calcium-binding DOMAIN 1490 1546 TB 6 DOMAIN 1563 1604 EGF-like 24 calcium-binding DOMAIN 1605 1646 EGF-like 25 calcium-binding DOMAIN 1651 1703 TB 7 DOMAIN 1721 1762 EGF-like 26 calcium-binding DOMAIN 1763 1804 EGF-like 27 calcium-binding DOMAIN 1805 1846 EGF-like 28 DOMAIN 1847 1885 EGF-like 29 calcium-binding DOMAIN 1886 1928 EGF-like 30 calcium-binding DOMAIN 1929 1968 EGF-like 31 calcium-binding DOMAIN 1969 2010 EGF-like 32 calcium-binding DOMAIN 2015 2068 TB 8 DOMAIN 2084 2125 EGF-like 33 calcium-binding DOMAIN 2126 2165 EGF-like 34 calcium-binding DOMAIN 2166 2206 EGF-like 35 calcium-binding DOMAIN 2207 2251 EGF-like 36 calcium-binding DOMAIN 2252 2293 EGF-like 37 calcium-binding DOMAIN 2298 2351 TB 9 DOMAIN 2363 2404 EGF-like 38 calcium-binding DOMAIN 2405 2445 EGF-like 39 calcium-binding DOMAIN 2446 2484 EGF-like 40 calcium-binding DOMAIN 2485 2527 EGF-like 41 calcium-binding DOMAIN 2528 2567 EGF-like 42 calcium-binding DOMAIN 2568 2609 EGF-like 43 calcium-binding DOMAIN 2610 2649 EGF-like 44 calcium-binding
EGF-like sequence regions
147 - 179 PICDRGCHNGGRCIGPNRCACVYGFMGPQCERD 247 - 288 DECQAVPGLCQGGSCVNMVGSFHCRCPVGHRLSDSSAACEDY 408 - 448 DICRHFTNLCLNGRCLPTPSSYRCECNVGYTQDVRGECIDV 449 - 488 DECTSSPCHHGDCVNIPGTYHCRCYPGFQATPTRQACVDV 489 - 530 DECIVSGGLCHLGRCVNTEGSFQCVCNAGFELSPDGKNCVDH 531 - 571 NECATSTMCVNGVCLNEDGSFSCLCKPGFLLAPGGHYCMDI 572 - 612 DECQTPGICVNGHCTNTEGSFRCQCLGGLAVGTDGRVCVDT 682 - 723 NECALDPEVCANGVCENLRGSYRCVCNLGYEAGASGKDCTDV 724 - 765 DECALNSLLCDNGWCQNSPGSYSCSCPPGFHFWQDTEICKDV 766 - 805 DECLSSPCVSGVCRNLAGSYTCKCGPGSRLDPSGTFCLDS 869 - 910 NECESFPGVCPNGRCVNTAGSFRCECPEGLMLDASGRLCVDV 986 - 1027 NECKVFPGLCTHGTCRNTVGSFHCACAGGFALDAQERNCTDI 1028 - 1070 DECRISPDLCGQGTCVNTPGSFECECFPGYESGFMLMKNCMDV 1071 - 1112 DECARDPLLCRGGTCTNTDGSYKCQCPPGHELTAKGTACEDI 1113 - 1154 DECSLSDGLCPHGQCVNVIGAFQCSCHAGFQSTPDRQGCVDI 1155 - 1195 NECRVQNGGCDVHCINTEGSYRCSCGQGYSLMPDGRACADV 1196 - 1237 DECEENPRVCDQGHCTNMPGGHRCLCYDGFMATPDMRTCVDV 1238 - 1279 DECDLNPHICLHGDCENTKGSFVCHCQLGYMVRKGATGCSDV 1280 - 1320 DECEVGGHNCDSHASCLNIPGSFSCRCLPGWVGDGFECHDL 1321 - 1361 DECVSQEHRCSPRGDCLNVPGSYRCTCRQGFAGDGFFCEDR 1362 - 1403 DECAENVDLCDNGQCLNAPGGYRCECEMGFDPTEDHRACQDV 1404 - 1444 DECAQGNLCAFGSCENLPGMFRCICNGGYELDRGGGNCTDI 1445 - 1485 NECADPVNCINGVCINTPGSYLCSCPQDFELNPSGVGCVDT 1563 - 1604 DECQELPGLCQGGDCVNTFGSFQCECPPGYHLSEHTRICEDI 1605 - 1646 DECSTHSGICGPGTCYNTLGNYTCVCPAEYLQVNGGNNCMDM 1721 - 1762 DECGEIPAICANGICINQIGSFRCECPAGFNYNSILLACEDV 1763 - 1804 DECGSRESPCQQNADCINIPGSYRCKCTRGYKLSPGGACVGR 1805 - 1846 NECREIPNVCSHGDCMDTEGSYMCLCHRGFQASADQTLCMDI 1847 - 1885 DECDRQPCGNGTCKNIIGSYNCLCFPGFVVTHNGDCVDF 1886 - 1928 DECTTLVGQVCRFGHCLNTAGSFHCLCQDGFELTADGKNCVDT 1929 - 1968 NECLSLAGTCLPGTCQNLEGSFRCICPPGFQVQSDHCIDI 1969 - 2010 DECSEEPNLCLFGTCTNSPGSFQCLCPPGFVLSDNGHRCFDT 2084 - 2125 NECAENPGVCTNGVCVNTDGSFRCECPFGYSLDFTGINCVDT 2126 - 2165 DECSVGHPCGQGTCTNVIGGFECACADGFEPGLMMTCEDI 2166 - 2206 DECSLNPLLCAFRCHNTEGSYLCTCPAGYTLREDGAMCRDV 2207 - 2251 DECADGQQDCHARGMECKNLIGTFACVCPPGMRPLPGSGEGCTDD 2252 - 2293 NECHAQPDLCVNGRCVNTAGSFRCDCDEGFQPSPTLTECHDI 2363 - 2404 DECRMLAHLCAHGECINSLGSFRCHCQAGYTPDATATTCLDM 2405 - 2445 DECSQVPKPCTFLCKNTKGSFLCSCPRGYLLEEDGRTCKDL 2446 - 2484 DECTSRQHNCQFLCVNTVGAFTCRCPPGFTQHHQACFDN 2485 - 2527 DECSAQPGPCGAHGHCHNTPGSFRCECHQGFTLVSSGHGCEDV 2528 - 2567 NECDGPHRCQHGCQNQLGGYRCSCPQGFTQHSQWAQCVDE 2568 - 2609 NECALSPPTCGSASCRNTLGGFRCVCPSGFDFDQALGGCQEV 2610 - 2649 DECAGRRGPCSYSCANTPGGFLCGCPQGYFRAGQGHCVSG
Function
"Fibrillin-3: Fibrillins are structural components of 10-12 nm extracellular calcium-binding microfibrils, which occur either in association with elastin or in elastin-free bundles. Fibrillin-containing microfibrils provide long-term force bearing structural support"